Shaymurzin M. Features of electromyographic pattern in early diagnostics of мyelino- and axonopathies in children with hereditary motosensory neuropathy

As a result of dissertation research children have the extended pictures of pathogeny, clinic and diagnostics of neurological displays of НMSN, theoretical generalization and new decision of scientific issue of the day is an early exposure of specific ENMG-маrkers of мyelino- and axonopathies is presented and ENMG-predictores of progrediation of pathological process at НMSN. What allowed to develop and offer the scientifically grounded approaches of nosotropic treatment of children from НMSN, directed on warning of invalidi-sation and deceleration of progrediation. Basic and initiation symtoms are presented neurological displays of НMSN for children depending on as НMSN. In neurological status of children from НMSN1 on 24,9% more frequent appear symptoms of distal muscular hy-potony and hypotrophy of legs, on 22,4% is deformation feet (pes cavus), on 22,3% is a decline of vibratiation sensitiveness, than for patients from НMSN2. Found out the specific ENMG-маrkers of мyelino- and axonopathies and ENMG-predictores of clinical progredia-tion of pathological process for children from НMSN. The scientifically grounded approaches of nosotropic treatment of children are developed and offered from НMSN, directed on warning of invalidisation and deceleration of progrediation.